Journal of Rheumatic Diseases

Table. 2.

Process of classifying GPA and MPA in patients without ANCA

Number AAV
Subtype
Sex/Age Fulfilling the ACR criteria for EGPA Histology compatible with GPA Histology compatible with MPA with GPA surrogate markers Histology compatible with MPA without GPA surrogate markers Biopsy sites
1 GPA M/54 No Yes Paranasal sinus
2 GPA F/62 No Yes Paranasal sinus
3 GPA F/66 No Yes Paranasal sinus
4 GPA F/45 No Yes Lungs
5 GPA F/79 No Yes Lungs
6 GPA F/58 No No Yes Kidneys
7 GPA F/20 No No Yes Kidneys
8 GPA M/49 No No Yes Kidneys
9 MPA F/62 No No No Yes Kidneys
10 MPA M/75 No No No Yes Kidneys
11 MPA F/47 No No No Yes Kidneys
12 MPA F/69 No No No Yes Kidneys
13 MPA F/56 No No No Yes Kidneys
14 MPA M/33 No No No Yes Kidneys
15 MPA F/50 No No No Yes Kidneys
16 MPA M/40 No No No Yes Kidneys
17 MPA F/57 No No No Yes Kidneys
18 MPA F/69 No No No Yes Kidneys
19 MPA M/70 No No No Yes Kidneys
20 MPA F/30 No No No Yes Nerve and skin
21 MPA F/60 No No No Yes Paranasal sinus
22 MPA F/34 No No No Yes Myocardium and nerve
23 MPA F/47 No No No Possible Skin
24 MPA F/50 No No No Possible Skin
25 MPA F/32 No No No Possible Skin

MPA: microscopic polyangiitis, GPA: granulomatosis with polyangiitis, AAV: ANCA-associated vasculitis, ANCA: antineutrophil cytoplasmic antibody, EMA: European Medicine Agency, ACR: American College of Rheumatology, EGPA: eosinophilic granulomatosis with polyangiitis.

J Rheum Dis 2022;29:40~45 https://doi.org/10.4078/jrd.2022.29.1.40
© J Rheum Dis