Acute Polymyositis/systemic Lupus Erythematosus Overlap Syndrome with Severe Subcutaneous Edema and Interstitial Lung Disease

U-ram Jin; Kyu-Sung Kwack; Kyung-Joo Park; Ji-Eun Kwon; Si-Yeon Kim; Ki-Chan Kim; Ga-Yong Ban; Ju-Yang Jung; Chang-Hee Suh; Hyoun-Ah Kim

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Case Report

J Rheum Dis 2014; 21(1): 25-29

Published online February 28, 2014

Acute Polymyositis/systemic Lupus Erythematosus Overlap Syndrome with Severe Subcutaneous Edema and Interstitial Lung Disease

U-ram Jin¹, Kyu-Sung Kwack², Kyung-Joo Park², Ji-Eun Kwon³, Si-Yeon Kim¹, Ki-Chan Kim¹, Ga-Yong Ban¹, Ju-Yang Jung¹, Chang-Hee Suh¹, Hyoun-Ah Kim¹

Author Info. +

Departments of Rheumatology¹, Radiology², Pathology³, Ajou University School of Medicine, Suwon, Korea

Correspondence to : Hyoun-Ah Kim

Received: March 12, 2013; Revised: May 10, 2013; Accepted: May 12, 2013

Abstract

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Abstract

Inflammatory myopathy is characterized by symmetrical proximal muscle weakness, elevated muscle enzyme levels and favorable response to glucocorticoids therapy. Although periorbital edema is a common manifestation of inflammatory myopathy, generalized subcutaneous edema is very rare. We report here a case of a 47-year-old female patient with acute polymyositis/systemic lupus eryth-ematosus overlap syndrome with generalized subcutaneous edema and interstitial lung disease. We aggressively treat-ed the disease with high-dose glucocorticoids, intravenous immunoglobulin, and immunosuppressive agents.

Keywords Inflammatory myopathy, Overlap syndrome, Subcutaneous edema, Interstitial lung disease

Article

Case Report

J Rheum Dis 2014; 21(1): 25-29

Published online February 28, 2014

Acute Polymyositis/systemic Lupus Erythematosus Overlap Syndrome with Severe Subcutaneous Edema and Interstitial Lung Disease

U-ram Jin¹, Kyu-Sung Kwack², Kyung-Joo Park², Ji-Eun Kwon³, Si-Yeon Kim¹, Ki-Chan Kim¹, Ga-Yong Ban¹, Ju-Yang Jung¹, Chang-Hee Suh¹, Hyoun-Ah Kim¹

Departments of Rheumatology¹, Radiology², Pathology³, Ajou University School of Medicine, Suwon, Korea

Correspondence to:Hyoun-Ah Kim

Received: March 12, 2013; Revised: May 10, 2013; Accepted: May 12, 2013

Abstract

Keywords: Inflammatory myopathy, Overlap syndrome, Subcutaneous edema, Interstitial lung disease

Abstract

Oct 01, 2024 Vol.31 No.4, pp. 191~263

COVER PICTURE

Ancestry-driven pathways for SLE-risk SNP-associated genes. The ancestry-driven key signaling pathways in Asians, Europeans, and African Americans were analyzed by enrichr (https://maayanlab.cloud/Enrichr/#libraries) using non-HLA SNP-associated genes. SLE: systemic lupus erythematosus, SNP: single-nucleotide polymorphism, JAK–STAT: janus kinase–signal transducers and activators of transcription, IFN: interferon gamma. (J Rheum Dis 2024;31:200-211)

Case Report

Acute Polymyositis/systemic Lupus Erythematosus Overlap Syndrome with Severe Subcutaneous Edema and Interstitial Lung Disease

Abstract

Article

Case Report

Acute Polymyositis/systemic Lupus Erythematosus Overlap Syndrome with Severe Subcutaneous Edema and Interstitial Lung Disease

Abstract

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